Читать книгу The Surgery of the Skull and Brain - Louis Bathe Rawling - Страница 50

Sincipital cephaloceles are usually quite small, but the occipital variety and those situated in the region of the anterior fontanelle frequently attain a great size (see Figs. 20-22).

Fig. 22. An Occipital Cephalocele. (For further description, see text.)

It is not always possible to determine whether the tumour consists of a mere outward protrusion of membranes (meningocele), or whether brain-matter enters into the formation of the tumour (meningo-encephalocele). Fluctuation, translucency, and pulsation are all points to be investigated. All these features are, however, deceptive, and several cases are on record in which operative measures were carried out under the impression that the surgeon had to deal with a pure meningocele, and in which it was afterwards found that brain-matter formed the basis of the swelling.

When the tumour is large, the skin adherent, when no pedicle is present, when fluctuation and pulsation are absent, and when the tumour is of firm consistency, then it is practically certain that brain-matter shares largely in the formation of the tumour. On the other hand, it is not unusual to find that the brain projects markedly outwards without resulting in any symptoms of brain irritation: fluctuation and pulsation are also not infallible signs, since the brain may occupy the base of the tumour, ‘corking-up’ the gap in the bone, or the brain may be so thinned by ventricular distension that a mere shell of cerebral matter lies beneath the scalp-covering.

Looking at the question from all points of view, it may be accepted that most cephaloceles contain either true brain-matter or the mixed epiblastic and mesoblastic elements described by Lyssenkow.

The following case serves to illustrate some of these facts:[9]—

The child was 3 months old, and presented a tumour, the size of an orange, situated between the occipital protuberance and the nape of the neck. The mass was pedunculated, the stalk being about the size of a four-shilling piece in diameter. It was soft, translucent, irreducible, and swelled up on coughing. An attempt at removal was carried out, and, after incising the outermost layers, three ounces of cerebro-spinal fluid escaped. A second tumour was then found occupying the base of the swelling. This was also punctured, more fluid escaping. Both sacs were cut away and the wound sewn up. Death occurred on the third day, preceded by convulsions, retraction of the head and neck, and high fever. The autopsy showed that the fontanelles were widely open, the anterior measuring 4 inches from side to side and 2¹⁄₂ from before backwards. The bones of the vault were markedly thinned. In the subdural space there was a quantity of fluid, and the cerebral substance was soft and diffluent, the convolutions flattened, and the ventricles distended. There was a broad gap in the occipital bone, extending downwards into the foramen magnum, and in this situation the cerebellum had bulged backwards into the protruding mass. (See Fig. 22).

For differential diagnosis, see p. 57.