Читать книгу The Peripheral T-Cell Lymphomas - Группа авторов - Страница 103

Primary cutaneous gamma–delta PTCL was originally classified under cutaneous panniculitis‐like T‐cell lymphoma [74], however, due to its gamma–delta phenotype and the aggressive nature of disease, it was recognized as a separate entity in the 2008 WHO classification [9, 75]. It accounts for approximately 1% of CTCLs and because of the rarity of this entity its exact incidence and specific risk factors are not well understood. While males and females are equally affected, the age of incidence ranges from 40 to 60 years [76]. Unlike other types of PTCL, the most common site of origin is oral mucosa, as gamma–delta T‐cells are more prevalent at mucosal sites [77].